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VOLUME 12 , ISSUE 1 ( January-June, 2022 ) > List of Articles

CASE REPORT

Congenital Cricopharyngeal Achalasia in an Infant Treated by External Cricopharyngeal Myotomy: A Case Report

S Vivek, Jayakumar R Menon, Manju E Issac, Jayanthy Pavithran

Keywords : Achalasia, Aspiration, Cricopharyngeus, Dysphagia, Myotomy

Citation Information : Vivek S, Menon JR, Issac ME, Pavithran J. Congenital Cricopharyngeal Achalasia in an Infant Treated by External Cricopharyngeal Myotomy: A Case Report. Int J Phonosurg Laryngol 2022; 12 (1):16-18.

DOI: 10.5005/jp-journals-10023-1230

License: CC BY-NC 4.0

Published Online: 30-07-2022

Copyright Statement:  Copyright © 2022; The Author(s).


Abstract

Congenital cricopharyngeal atresia is a rare but serious cause of dysphagia in infants. The failure of the cricopharyngeus muscle (CPM) to adequately relax on food intake is considered as the cause. This condition usually presents early in life with symptoms that include regurgitation, nasopharyngeal reflux, aspiration, choking episodes, and failure to thrive. Videofluoroscopy helps to clinch the diagnosis, demonstrating a prominent cricopharyngeal bar in most cases. This describes the case report of a male infant who presented with cricopharyngeal achalasia (CPA) and underwent open cricopharyngeal myotomy at 6 months of age, leading to the resolution of symptoms.

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