Citation Information :
Vivek S, Menon JR, Issac ME, Pavithran J. Congenital Cricopharyngeal Achalasia in an Infant Treated by External Cricopharyngeal Myotomy: A Case Report. Int J Phonosurg Laryngol 2022; 12 (1):16-18.
Congenital cricopharyngeal atresia is a rare but serious cause of dysphagia in infants. The failure of the cricopharyngeus muscle (CPM) to adequately relax on food intake is considered as the cause. This condition usually presents early in life with symptoms that include regurgitation, nasopharyngeal reflux, aspiration, choking episodes, and failure to thrive. Videofluoroscopy helps to clinch the diagnosis, demonstrating a prominent cricopharyngeal bar in most cases. This describes the case report of a male infant who presented with cricopharyngeal achalasia (CPA) and underwent open cricopharyngeal myotomy at 6 months of age, leading to the resolution of symptoms.
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