International Journal of Phonosurgery & Laryngology

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VOLUME 11 , ISSUE 1 ( January-June, 2021 ) > List of Articles


Supraglottic Laryngeal Paraganglioma: A Rare Entity

Abhinav Agarwal, Ruchika Juneja

Keywords : Laryngeal paraganglioma, Laryngofissure, Neuroendocrine tumor, Zellballen pattern

Citation Information : Agarwal A, Juneja R. Supraglottic Laryngeal Paraganglioma: A Rare Entity. Int J Phonosurg Laryngol 2021; 11 (1):25-28.

DOI: 10.5005/jp-journals-10023-1192

License: CC BY-NC 4.0

Published Online: 18-08-2021

Copyright Statement:  Copyright © 2021; The Author(s).


Aim and objective: To discuss a rare case of supraglottic paraganglioma presenting as stridor and its management. Background: Paragangliomas are tumors anatomically arising from the dispersed neuroendocrine system (paraganglia), derived from the neural crest of the autonomic ganglia and characterized by similar neurosecretory cells. They are rarely seen in larynx. Most cases have polypoidal presentation in the endolarynx and diagnosis is usually confirmed after histopathology. Case description: We present a rare case of laryngeal paraganglioma in which the patient presented with stridor and was successfully treated by open laryngofissure approach leading to excision of the tumor with complete preservation of laryngeal function. Conclusion: Paragangliomas of the larynx are vascular benign tumors and can have varied presentations. Familiarity with these rare masses is essential for the treating otolaryngologist to prevent an inadvertent biopsy. A carefully selected surgical approach helps preserve adequate laryngeal function and decreases the risk of recurrence.

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